Tehran University of Medical Sciences Case Reports in Clinical Practice 2538-2683 9 6 2025 07 01 257 265 Hamidreza Aghadoost Department of Neurosurgery, School of Medicine, Kashan University of Medical Sciences, Kashan, Iran. Ghazaleh Salehabadi Department of Radiology, School of Medicine, Iran University of Medical Sciences, Tehran, Iran. Abdolnaser Farzan Department of Neurosurgery, Educational and Therapeutic Center, Mofid Children’s Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran. Emad Tavakkoli Department of Neurosurgery, School of Medicine, Shahid Beheshti University of Medical Sciences, Tehran, Iran. 2025 03 02 2025 05 06 The larval stages of Echinococcus granulosus cause hydatidosis or hydatid disease, which primarily affects children worldwide. It primarily impacts the lungs and liver, but brain hydatidosis is an infrequent condition in the pediatric population. This condition presents with non-specific signs and symptoms. Intracranial hydatid cysts can be diagnosed through brain magnetic resonance imaging (MRI) and histopathological examination of the specimen. In this report, we describe a case of a 4-year-old boy diagnosed with a temporoparietooccipital brain hydatid cyst. The MRI revealed a thin-walled cystic lesion in the left temporoparietooccipital lobe. It  showed a significant mass effect and midline shift, with no abnormal wall or solid enhancement and no surrounding edema. Based on these imaging findings, a diagnosis of a brain hydatid cyst was made. The patient underwent surgery, during which the cyst was removed entirely without rupture. Histopathological examination confirmed the diagnosis of a brain hydatid cyst. The patient had a smooth postoperative recovery, began treatment with albendazole, and was discharged in improved health. https://crcp.tums.ac.ir/index.php/crcp/article/view/1028 https://crcp.tums.ac.ir/index.php/crcp/article/download/1028/697