Tehran University of Medical Sciences Case Reports in Clinical Practice 2538-2683 3 3 2019 01 15 73 77 EN Payam Saadat Department of Neurology, Mobility Impairment Disorders Research Center, Babol University of Medical Sciences, Babol, Iran. Tahereh Hejazian Department of Infectious Diseases, School of Medicine, Mobility Impairment Disorders Research Center, Babol University of Medical Sciences, Babol, Iran. Reza Mohseni Ahangar Clinical Research Development Unit of Rouhani Hospital, Babol University of Medical Sciences, Babol, Iran. 2018 05 13 2018 09 30 Fahr’s syndrome is a rare neurodegenerative disorder. Bilateral basal ganglia and dentate nuclei of the cerebellum are involved in this disorder and deposition of calcium is the hallmark of this syndrome. It has been recognized as a sporadic or inherited disease with variable presentations. In this article, we report a 40-year-old man with incidentally discovered brain calcifcation as the sole manifesation of Fahr’s syndrome. A 40-year-old male without any comorbidities was presented with brain calcifcation that was found incidentally. Brain imaging revealed symmetric calcifcations in bilateral basal ganglia, internal capsules, and cerebral white matter. This pattern of calcifcation is highly suspicious of Fahr’s syndrome. Other pathologic processes that could lead to intracranial calcifcation were excluded. We present a young patient with sporadic and asymptomatic Fahr’s syndrome after ruling out abnormalities of known calcium metabolism and developmental defects. https://crcp.tums.ac.ir/index.php/crcp/article/view/195 https://crcp.tums.ac.ir/index.php/crcp/article/download/195/277