Tehran University of Medical Sciences Case Reports in Clinical Practice 2538-2683 7 2 2022 09 26 86 90 Marzieh Pazoki Department of Pulmonary Medicine, Sina Hospital, Tehran University of Medical Sciences, Tehran, Iran. Elham Nazar Department of Pathology, Sina Hospital, Tehran University of Medical Sciences, Tehran, Iran. Behnaz Jahanbin Department of Pathology, Imam Khomeini Complex Hospital, Tehran University of Medical Sciences, Tehran, Iran. 2021 05 31 2021 07 14 Benign metastasizing leiomyoma of the lung which is categorized by the growth of uterine leiomyoma in the lung is an extremely exceptional disease.We report a 39-year-old woman who had a previous history of uterine leiomyoma. Chest computed tomography (CT) scan exhibited round nodules well-defined margins in both lungs. Thoracoscopic partial resection of the lung was done. Pathological and immunohistochemical examination showed that neoplastic tissue composed of spindle-shaped smooth muscle cells, compatible with uterine leiomyoma. Thus, these tumors can be reflected to be lung metastases from a uterine leiomyoma (benign metastasizing leiomyoma).It is an uncommon condition but it would be careful in women of re- productive age with a past medical history of uterine leiomyoma, who existing with pulmonary nodules. https://crcp.tums.ac.ir/index.php/crcp/article/view/549