Tehran University of Medical Sciences Case Reports in Clinical Practice 2538-2683 1 4 2017 06 24 102 105 EN Farzad Allameh Department of Urology, Shohada-e-Tajrish Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran. Hamidreza Qashqai Department of Urology, Shohada-e-Tajrish Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran. Farideh Mousavi Department of Pediatric Oncology, Shohada-e-Tajrish Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran. Ali Halimi Asl Department of Pediatric Oncology, Shohada-e-Tajrish Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran. Amirhossein Rahavian Department of Urology, Shohada-e-Tajrish Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran. 2016 04 08 2016 09 24 A thirteen-year-old boy with a right flank mass and painless gross hematuria is presented. The patient underwent open biopsy and the result was a huge primitive neuroectodermal tumor (PNET) of right kidney. Radical nephrectomy was performed for him and the treatment process continued with systemic chemotherapy. https://crcp.tums.ac.ir/index.php/crcp/article/view/57 https://crcp.tums.ac.ir/index.php/crcp/article/download/57/56