Tehran University of Medical Sciences Case Reports in Clinical Practice 2538-2683 9 1 2024 10 22 35 38 EN Maryam Ghffarirahbar Department of Internal Medicine, School of Medicine, Hazrat- e Rasool General Hospital, Iran University of Medical sciences (IUMS), Tehran, Iran. Tahereh ZaroukAhimahalle Department of Internal Medicine, School of Medicine, Hazrat- e Rasool General Hospital, Iran University of Medical sciences (IUMS), Tehran, Iran. Maedeh Olya Department of Internal Medicine, School of Medicine, Hazrat- e Rasool General Hospital, Iran University of Medical sciences (IUMS), Tehran, Iran. 2024 05 22 2024 06 11 Distal renal tubular acidosis (RTA1) is a rare disease. It confirms the lab’s data and rules out other differential diagnoses. Late evaluation can interfere with healthy development. We explain a 38-year-old patient with a late and accidental RTA1 diagnosis. Correct treatment with alkali consumption and potassium citrate improves her general condition and eliminates further weakness attacks. Early diagnosis is crucial for patient development and morbidity avoidance with accurate treatments. https://crcp.tums.ac.ir/index.php/crcp/article/view/952 https://crcp.tums.ac.ir/index.php/crcp/article/download/952/631