Anesthetic Considerations of Patient with Parry Romberg Syndrome

  • Sussan Soltani Mohammadi Department of Anesthesiology, Pain and Intensive Care Medicine, Shariati Hospital, Tehran University of Medical Sciences, Tehran, Iran.
  • Farideh Toorany Sina-Shemiran Plastic Surgery Center, Tehran, Iran.
  • Abdolrahim Shahhosseini Department of Ophthalmology, Ayatollah Kashani Hospital, Tehran, Iran.
Keywords: Anesthesia, Hemifacial atrophy, Progressive hemifacial atrophy, Scleroderma

Abstract

Parry Romberg syndrome is a rare progressive degenerative disease characterized by unilateral atrophy affecting the skin, connective tissue, muscle, and bone, typically occurs in children and young adults. The end result is facial asymmetry associated with other skin, dental, visual, cardiovascular, and neurological disorders that ceases without apparent cause after a highly variable period. Inconsistency in the pattern of atrophy and multisystem involvement make intraoperative anesthetic management of these patients a challenge for anesthesiologists. We present a case of Parry Romberg syndrome and her associated clinical findings with specific attention to the anesthetic consideration of this disease.

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Published
2018-07-24
How to Cite
1.
Soltani Mohammadi S, Toorany F, Shahhosseini A. Anesthetic Considerations of Patient with Parry Romberg Syndrome. CRCP. 3(1):26-9.
Section
Case Report(s)