Night View of Eiffel Tower’- Radiological Sign of Chronic Idiopathic Hypertrophic Pachymeningitis: A Case Report
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Abstract
Chronic idiopathic hypertrophic pachymeningitis (IHP) is a rare inflammatory entity with unknown etiopathogenesis, resulting in dural thickening and fibrosis. This mimics the illuminated night view of the Eiffel tower on contrast-enhanced MRI. The authors report a characteristic MRI sign of chronic IHP on contrast-enhanced MRI. The authors present a case of a 30-year-old male presenting with a headache for the past 3 years with recent aggravation of symptoms. Laboratory and imaging results were reviewed. Follow-up imaging with ongoing treatment was also reviewed. The etiology could not be determined even after extensive investigations. Contrast-enhanced MRI revealed diffuse enhancing thickening of the pachymeninges along the posterior cerebral hemispheres, falx cerebri, and tentorium cerebelli, giving the typical ‘Night view of the Eiffel tower’ appearance on coronal images. There was cerebral venous sinus thrombosis secondary to IHP. The patient was treated with corticosteroids and anticoagulants. The follow-up scan revealed reduced thickness and enhancement of the meninges.
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| Issue | Vol 8 No 5 (2023): September-October | |
| Section | Case Report(s) | |
| DOI | https://doi.org/10.18502/crcp.v8i5.15259 | |
| Keywords | ||
| Chronic idiopathic hypertrophic pachymeningitis (IHP) Eiffelby-night appearance Chronic headache | ||
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