Case Reports in Clinical Practice 2016. 1(4):102-105.

Primitive Neuroectodermal Tumor (PNET): a Rare Tumor in Differential Diagnosis of Renal Mass in Adolescences
Farzad Allameh, Hamidreza Qashqai, Farideh Mousavi, Ali Asghar Halimi Asl, Amirhossein Rahavian


A thirteen-year-old boy with a right flank mass and painless gross hematuria is presented. The patient underwent open biopsy and the result was a huge primitive neuroectodermal tumor (PNET) of right kidney. Radical nephrectomy was performed for him and the treatment process continued with systemic chemotherapy.


PNET; Renal mass; Biopsy; Metastasis

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Hamidi N, Esen B, Kivrak H, Sertcelik A, Gulpinar O. A large and metastatic primitive neuroectodermal tumor of the kidney. Turk J Urol 2015; 41(3): 152-4.

Chu WC, Reznikov B, Lee EY, Grant RM, Cheng FW, Babyn P. Primitive neuroectodermal tumour (PNET) of the kidney: a rare renal tumour in adolescents with seemingly characteristic radiological features. Pediatr Radiol 2008; 38(10): 1089-94.

Saxena R, Sait S, Mhawech-Fauceglia P. Ewing sarcoma/primitive neuroectodermal tumor of the kidney: a case report. Diagnosed by immunohistochemistry and molecular analysis. Ann Diagn Pathol 2006; 10(6): 363-6.

Sebire NJ, Vujanic GM. Paediatric renal tumours: recent developments, new entities and pathological features. Histopathology

; 54(5): 516-28.

Chang F. Desmoplastic small round cell tumors: cytologic, histologic, and immunohistochemical features. Arch Pathol Lab Med 2006; 130(5): 728-32.

Gerald WL, Rosai J. Case 2 Desmoplastic Small Cell Tumor with Divergent Differentiation. Pediatr Pathol 1989; 9(2): 177-83.

Lae ME, Roche PC, Jin L, Lloyd RV, Nascimento AG. Desmoplastic small round cell tumor: a clinicopathologic, immunohistochemical, and molecular study of 32 tumors. Am J Surg Pathol 2002; 26(7): 823-35.

Sawyer JR, Tryka AF, Lewis JM. A novel reciprocal chromosome translocation t(11;22)(p13;q12) in an intraabdominal desmoplastic small round-cell tumor. Am J Surg Pathol 1992; 16(4): 411-6.

Birch JM, Breslow N. Epidemiologic features of Wilms tumor. Hematol Oncol Clin North Am 1995; 9(6): 1157-78.

Vujanic GM, Kelsey A, Mitchell C, Shannon RS, Gornall P. The role of biopsy in the diagnosis of renal tumors of childhood: Results of the UKCCSG Wilms tumor study 3. Med Pediatr Oncol 2003; 40(1): 18-22.

Pomara G, Cappello F, Cuttano MG, Rappa F, Morelli G, Mancini P, et al. Primitive Neuroectodermal Tumor (PNET) of the kidney: a case report. BMC Cancer 2004; 4: 3.

Mandal PK, Mukherjee S, Roy S, Bhattacharyya NK. PNET of kidney: Report of four cases. Indian J Med Paediatr Oncol 2012; 33(2): 130-3.

Kairouani M, Mokrim M, Mellas N, Khennoussi B, M'rabti HE, Boutayeb S, et al. Metastatic Ewing's sarcoma/PNET of kidney in 40 year old patient. Int J Surg Case Rep

; 3(6): 215-7.


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