Primitive Neuroectodermal Tumor (PNET): A Rare Tumor in Differential Diagnosis of Renal Mass in Adolescences
,
Abstract
A thirteen-year-old boy with a right flank mass and painless gross hematuria is presented. The patient underwent open biopsy and the result was a huge primitive neuroectodermal tumor (PNET) of right kidney. Radical nephrectomy was performed for him and the treatment process continued with systemic chemotherapy.
Hamidi N, Esen B, Kivrak H, Sertcelik A, Gulpinar O. A large and metastatic primitive neuroectodermal tumor of the kidney. Turk J Urol 2015; 41(3): 152-4.
Chu WC, Reznikov B, Lee EY, Grant RM, Cheng FW, Babyn P. Primitive neuroectodermal tumour (PNET) of the kidney: a rare renal tumour in adolescents with seemingly characteristic radiological features. Pediatr Radiol 2008; 38(10): 1089-94.
Saxena R, Sait S, Mhawech-Fauceglia P. Ewing sarcoma/primitive neuroectodermal tumor of the kidney: a case report. Diagnosed by immunohistochemistry and molecular analysis. Ann Diagn Pathol 2006; 10(6): 363-6.
Sebire NJ, Vujanic GM. Paediatric renal tumours: recent developments, new entities and pathological features. Histopathology
; 54(5): 516-28.
Chang F. Desmoplastic small round cell tumors: cytologic, histologic, and immunohistochemical features. Arch Pathol Lab Med 2006; 130(5): 728-32.
Gerald WL, Rosai J. Case 2 Desmoplastic Small Cell Tumor with Divergent Differentiation. Pediatr Pathol 1989; 9(2): 177-83.
Lae ME, Roche PC, Jin L, Lloyd RV, Nascimento AG. Desmoplastic small round cell tumor: a clinicopathologic, immunohistochemical, and molecular study of 32 tumors. Am J Surg Pathol 2002; 26(7): 823-35.
Sawyer JR, Tryka AF, Lewis JM. A novel reciprocal chromosome translocation t(11;22)(p13;q12) in an intraabdominal desmoplastic small round-cell tumor. Am J Surg Pathol 1992; 16(4): 411-6.
Birch JM, Breslow N. Epidemiologic features of Wilms tumor. Hematol Oncol Clin North Am 1995; 9(6): 1157-78.
Vujanic GM, Kelsey A, Mitchell C, Shannon RS, Gornall P. The role of biopsy in the diagnosis of renal tumors of childhood: Results of the UKCCSG Wilms tumor study 3. Med Pediatr Oncol 2003; 40(1): 18-22.
Pomara G, Cappello F, Cuttano MG, Rappa F, Morelli G, Mancini P, et al. Primitive Neuroectodermal Tumor (PNET) of the kidney: a case report. BMC Cancer 2004; 4: 3.
Mandal PK, Mukherjee S, Roy S, Bhattacharyya NK. PNET of kidney: Report of four cases. Indian J Med Paediatr Oncol 2012; 33(2): 130-3.
Kairouani M, Mokrim M, Mellas N, Khennoussi B, M'rabti HE, Boutayeb S, et al. Metastatic Ewing's sarcoma/PNET of kidney in 40 year old patient. Int J Surg Case Rep
; 3(6): 215-7.
| Files | ||
| Issue | Vol 1 No 4 (2016): Autumn | |
| Section | Case Report(s) | |
| Keywords | ||
| PNET Renal mass Biopsy Metastasis | ||
| Rights and permissions | |
|
This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License. |
